Journal of Education and Health Promotion

Health-related quality of life of hemophilics and its possible correlates: A perspective in health promotion and disability prevention

Document Type : Original Article

Authors

. Soumyaneel Das
. Rabindra Nath Roy
. Dilip Kumar Das
. Amitava Chakraborty
. Raston Mondal
Abstract
BACKGROUND: Clinical evaluations are not sufficient to adequately characterize the morbidity
associated with hemophilia. Quality of life (QoL) of hemophilics and associated factors is not well
explored in Indian research. The present study aimed to measure the QoL in hemophilics and its
association with socio‑demographic characteristics and other characteristics.
MATERIALS AND METHODS: A cross‑sectional study was conducted during June–November 2018.
Two hundred and one hemophilics (age ≥ 4 years) were interviewed with a pre‑tested schedule for
sociodemographic and other relevant variables. QoL was measured by Haemo‑QoL questionnaire for
different pediatric age groups and Haem‑A‑QoL questionnaire for adults and assigned health‑related
QoL scores. Score achieved in each dimension as well as total scores were transformed on scales
ranging from 0 to 100, high values indicate high impairment of QoL. Hemophilic arthropathy was
assessed using the World Federation of Hemophilia Joint Scores. One‑way ANOVA, independent
t‑test, Kruskal–Wallis test, and Spearman correlation analyses were performed using SPSS
version 16.
RESULTS: Mean Haemo‑QoL scores for 4–7 years, 8–12 years, 13–16 years, and >16 years were
43.92 ± 8.09, 37.37 ± 8.62, 32.79 ± 6.66, and 45.92 ± 6.30, respectively. Significant difference was
noted for QoL scores across different age groups, grades of severity, educational, occupational
categories, socioeconomic status classes, marital status, and presence or absence of target joint. Total
QoL scores, as well as scores in some of the dimensions, showed a significant positive correlation
with the World Federation of Hemophilia joint scores by Spearman correlation analysis.
CONCLUSIONS: Improvement of the joint health status by regular physiotherapy is needed to
improve the QoL of hemophilics.

Keywords

Haemo‑quality of life score
health‑related quality of life
hemophilics
target joint
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Journal of Education and Health Promotion
Volume 9, Issue 12
December 2019
Pages 1-6

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